<?xml version='1.0' encoding='utf-8'?>
<?xml-stylesheet type="text/xsl" href="/v2/static/oai2.xsl"?>
<OAI-PMH xmlns="http://www.openarchives.org/OAI/2.0/" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xsi:schemaLocation="http://www.openarchives.org/OAI/2.0/ http://www.openarchives.org/OAI/2.0/OAI-PMH.xsd">
  <responseDate>2026-07-23T11:11:35Z</responseDate>
  <request identifier="oai:figshare.com:article/14822463" metadataPrefix="oai_datacite" verb="GetRecord">https://api.figshare.com/v2/oai</request>
  <GetRecord>
    <record>
      <header>
        <identifier>oai:figshare.com:article/14822463</identifier>
        <datestamp>2021-07-07T13:27:06Z</datestamp>
        <setSpec>category_24382</setSpec>
        <setSpec>category_24403</setSpec>
        <setSpec>category_24892</setSpec>
        <setSpec>portal_549</setSpec>
        <setSpec>item_type_3</setSpec>
        <setSpec>month_year_07_2021</setSpec>
      </header>
      <metadata>
        <resource xmlns="http://datacite.org/schema/kernel-4" xsi:schemaLocation="http://datacite.org/schema/kernel-4 http://schema.datacite.org/meta/kernel-4.3/metadata.xsd">
          <identifier identifierType="DOI">10.5522/04/14822463.v2</identifier>
          <alternateIdentifiers>
            <alternateIdentifier alternateIdentifierType="URL">https://figshare.com/articles/dataset/CSF_Nfl_results_CLN2_disease/14822463</alternateIdentifier>
          </alternateIdentifiers>
          <relatedIdentifiers>
            <relatedIdentifier relatedIdentifierType="URL" relationType="HasPart">https://ndownloader.figshare.com/files/28531722</relatedIdentifier>
            <relatedIdentifier relatedIdentifierType="URL" relationType="HasPart">https://ndownloader.figshare.com/files/31656080</relatedIdentifier>
          </relatedIdentifiers>
          <creators>
            <creator>
              <creatorName>Heywood, Wendy</creatorName>
              <givenName>Wendy</givenName>
              <familyName>Heywood</familyName>
            </creator>
            <creator>
              <creatorName>Iwan, Katharina</creatorName>
              <givenName>Katharina</givenName>
              <familyName>Iwan</familyName>
            </creator>
            <creator>
              <creatorName>Gissen, Paul</creatorName>
              <givenName>Paul</givenName>
              <familyName>Gissen</familyName>
            </creator>
            <creator>
              <creatorName>Zetterberg, Henrik</creatorName>
              <givenName>Henrik</givenName>
              <familyName>Zetterberg</familyName>
            </creator>
            <creator>
              <creatorName>Heslegrave, Amanda</creatorName>
              <givenName>Amanda</givenName>
              <familyName>Heslegrave</familyName>
            </creator>
            <creator>
              <creatorName>Patel, Nina</creatorName>
              <givenName>Nina</givenName>
              <familyName>Patel</familyName>
            </creator>
            <creator>
              <creatorName>Borisova, Mina</creatorName>
              <givenName>Mina</givenName>
              <familyName>Borisova</familyName>
            </creator>
            <creator>
              <creatorName>lee, laura</creatorName>
              <givenName>laura</givenName>
              <familyName>lee</familyName>
            </creator>
            <creator>
              <creatorName>Bower, Rebecca</creatorName>
              <givenName>Rebecca</givenName>
              <familyName>Bower</familyName>
            </creator>
            <creator>
              <creatorName>Mole, Sara</creatorName>
              <givenName>Sara</givenName>
              <familyName>Mole</familyName>
            </creator>
            <creator>
              <creatorName>Mills, Philippa</creatorName>
              <givenName>Philippa</givenName>
              <familyName>Mills</familyName>
            </creator>
            <creator>
              <creatorName>Mills, Kevin</creatorName>
              <givenName>Kevin</givenName>
              <familyName>Mills</familyName>
            </creator>
          </creators>
          <titles>
            <title><![CDATA[CSF Nfl results CLN2 disease]]></title>
          </titles>
          <subjects>
            <subject>Plant cell and molecular biology</subject>
            <subject>Animal cell and molecular biology</subject>
            <subject>Other biomedical and clinical sciences not elsewhere classified</subject>
            <subject>CLN2 disease</subject>
            <subject>neurofilament light</subject>
            <subject>enzyme replacement therapies</subject>
            <subject>Pediatric brains</subject>
            <subject>Molecular Biology</subject>
            <subject>Medicine</subject>
          </subjects>
          <dates>
            <date dateType="Created">2021-12-03</date>
            <date dateType="Updated">2021-12-03</date>
          </dates>
          <resourceType resourceTypeGeneral="Dataset">Dataset</resourceType>
          <publicationYear>2021</publicationYear>
          <publisher>University College London</publisher>
          <rightsList>
            <rights rightsURI="https://creativecommons.org/publicdomain/zero/1.0/" rightsIdentifier="CC0"/>
            <rights rightsURI="http://purl.org/coar/access_right/c_abf2" rightsIdentifier="open access"/>
          </rightsList>
          <descriptions>
            <description descriptionType="Abstract"><![CDATA[Dataset updated with alternative patient numbering to match manuscript. Excel data set of longditudinal CSF Nfl measurments (pg/ml) for pediatric patients undergoing ERT. <div>The collection of samples for this study has ethical approval
(13/LO/0168; IRAS ID 95005; London-Bloomsbury Research Ethics Committee) and
Health Research Authority (HRA) approval and all participants provided informed written
consent<br></div><div>CSF NfL protein concentration was measured on a Simoa HD-X analyser
using the Simoa NF-light Advantage assay kit (Quanterix, Billerica, MA) after
being diluted 100x. <br></div>]]></description>
          </descriptions>
        </resource>
      </metadata>
    </record>
  </GetRecord>
</OAI-PMH>
